先(Xian)天(Tian)性(Xing)白(Bai)内(Nei)障(Zhang)是(Shi)儿(?)童(Tong)常(Chang)见(Jian)眼(Yan)病(Bing),(?)为(Wei)出(Chu)生(Sheng)时(Shi)或(Huo)出(Chu)生(Sheng)后(Hou)第(Di)一(Yi)年(Nian)内(Nei)发(Fa)生(Sheng)的(De)晶(Jing)状(Zhuang)体(Ti)混(Hun)浊(Zhuo),(?)可(Ke)以(Yi)为(Wei)家(Jia)族(Zu)性(Xing)的(De)或(Huo)散(San)发(Fa)的(De);(?)可(Ke)以(Yi)伴(Ban)发(Fa)或(Huo)不(Bu)伴(Ban)发(Fa)其(Qi)他(Ta)眼(Yan)部(Bu)异(Yi)常(Chang)或(Huo)遗(Yi)传(Chuan)性(Xing)和(He)系(Xi)统(Tong)性(Xing)疾(Ji)病(Bing)。(?)先(Xian)天(Tian)性(Xing)白(Bai)内(Nei)障(Zhang)是(Shi)造(Zao)成(Cheng)儿(?)童(Tong)致(Zhi)盲(Mang)和(He)弱(Ruo)视(Shi)的(De)重(Zhong)要(Yao)原(Yuan)因(Yin)。(?)
【(?)病(Bing)因(Yin)】(?)各(Ge)种(Zhong)影(Ying)响(Xiang)胎(Tai)儿(?)晶(Jing)状(Zhuang)体(Ti)发(Fa)育(Yu)的(De)因(Yin)素(Su)都(Du)可(Ke)能(Neng)引(Yin)起(Qi)先(Xian)天(Tian)性(Xing)白(Bai)内(Nei)障(Zhang):(?)
1.遗(Yi)传(Chuan):(?)约(Yue)1/3患(Huan)者(Zhe)与(Yu)遗(Yi)传(Chuan)有(You)关(Guan)。(?)常(Chang)见(Jian)为(Wei)常(Chang)染(Ran)色(Se)体(Ti)显(Xian)性(Xing)遗(Yi)传(Chuan)。(?)如(Ru)伴(Ban)有(You)眼(Yan)部(Bu)其(Qi)他(Ta)先(Xian)天(Tian)异(Yi)常(Chang),(?)则(Ze)常(Chang)由(You)主(Zhu)要(Yao)异(Yi)常(Chang)的(De)遗(Yi)传(Chuan)方(Fang)式(Shi)所(Suo)决(Jue)定(Ding),(?)通(Tong)常(Chang)是(Shi)常(Chang)染(Ran)色(Se)体(Ti)隐(Yin)性(Xing)遗(Yi)传(Chuan)或(Huo)伴(Ban)性(Xing)遗(Yi)传(Chuan)。(?)
2.病(Bing)毒(Du)感(Gan)染(Ran):(?)母(Mu)亲(Qin)怀(Huai)孕(Yun)头(Tou)3个(Ge)月(Yue)宫(Gong)内(Nei)病(Bing)毒(Du)性(Xing)感(Gan)染(Ran),(?)如(Ru)风(Feng)疹(Zhen)、(?)疱(Pao)病(Bing)毒(Du)感(Gan)染(Ran)、(?)腮(Sai)腺(Xian)炎(Yan)、(?)麻(Ma)疹(Zhen)、(?)水(Shui)痘(Dou)等(Deng),(?)可(Ke)引(Yin)起(Qi)胎(Tai)儿(?)的(De)晶(Jing)状(Zhuang)体(Ti)混(Hun)浊(Zhuo)。(?)这(Zhe)是(Shi)由(You)于(Yu)此(Ci)时(Shi)晶(Jing)状(Zhuang)体(Ti)囊(Nang)膜(Mo)还(Huan)没(Mei)有(You)发(Fa)育(Yu)有(You)效(Xiao),(?)不(Bu)能(Neng)抵(Di)御(Yu)病(Bing)毒(Du)侵(Qin)犯(Fan),(?)而(?)且(Qie)晶(Jing)状(Zhuang)体(Ti)蛋(Dan)白(Bai)合(He)成(Cheng)活(Huo)跃(Yue),(?)对(Dui)病(Bing)毒(Du)感(Gan)染(Ran)敏(Min)感(Gan)。(?)
3.药(Yao)物(Wu)和(He)放(Fang)射(She)线(Xian):(?)母(Mu)亲(Qin)怀(Huai)孕(Yun)期(Qi),(?)特(Te)别(Bie)怀(Huai)孕(Yun)头(Tou)3个(Ge)月(Yue)内(Nei)应(Ying)用(Yong)一(Yi)些(Xie)药(Yao)物(Wu),(?)如(Ru)全(Quan)身(Shen)应(Ying)用(Yong)糖(Tang)皮(Pi)质(Zhi)激(Ji)素(Su),(?)一(Yi)些(Xie)抗(Kang)生(Sheng)素(Su),(?)特(Te)别(Bie)是(Shi)磺(Huang)胺(An)类(Lei)药(Yao)物(Wu),(?)或(Huo)暴(Bao)露(Lu)于(Yu)X线(Xian)。(?)
4.全(Quan)身(Shen)疾(Ji)病(Bing):(?)母(Mu)亲(Qin)怀(Huai)孕(Yun)期(Qi)患(Huan)有(You)代(Dai)谢(Xie)性(Xing)疾(Ji)病(Bing),(?)如(Ru)糖(Tang)尿(Niao)病(Bing)、(?)甲(Jia)状(Zhuang)腺(Xian)机(Ji)能(Neng)不(Bu)足(Zu)、(?)营(Ying)养(Yang)和(He)维(Wei)生(Sheng)素(Su)极(Ji)度(Du)缺(Que)乏(Fa)等(Deng)。(?)